Opa1 overexpression protects from early onset Mpv17-/--related mouse kidney disease
M. Zeviani, M. Luna-Sanchez, C. Beninca, R. Cerutti, A. Yeats, L. Scorrano, C. Viscomi, G. Brea Calvo
This study shows that moderate Opa1 overexpression in Mpv17-/- mice delays kidney disease progression by preserving mitochondrial structure and function.
bioRxiv · Mar 18, 2020Pathology