A PATHOGENIC NFKB2 VARIANT CAUSES COMBINED IMMUNODEFICIENCY WITH THYMIC AND PERIPHERAL LYMPHOID DEFECTS IN RATS
Séverine Remy, Laurent Tesson, Claire Usal, Marie Massoda, Séverine Ménoret, Irina Proekt, David Yu, Axel You, Matthieu Giraud, Mark Stuart Anderson, Ignacio Anegón
This study characterizes a rat model with a NFKB2 mutation, revealing systemic immunodeficiency with thymic and peripheral lymphoid defects.
bioRxiv · Oct 8, 2026 · PreprintImmunology