Myosin Heavy Chain Converter Domain Mutations Drive Early-Stage Changes in Extracellular Matrix Dynamics in Hypertrophic Cardiomyopathy
J. Hsieh, K. Becklin, S. Givens, E. R. Komosa, J. E. Abrahante Llorens, F. Kamdar, B. S. Moriarity, B. R. Webber, B. N. Singh, B. M. Ogle
This study identifies early-stage ECM dysregulation in HCM caused by MYH7/MYH6 mutations using hiPSC-derived cardiomyocytes.
bioRxiv · Apr 5, 2022Bioengineering