BiochemistrybioRxivPreprint
A Topological Switch Enables Misfolding of the Cystic Fibrosis Transmembrane Conductance Regulator
Daniel Scholl, Maud Sigoillot, Marie Overtus…·Cédric Govaerts
This study identifies a topological switch in CFTR's NBD1 domain that regulates channel function and contributes to misfolding in F508del-CFTR.
DOI 10.1101/2020.07.09.195099