PhysiologybioRxivPreprint
Role Of Chymotrypsin-Like Elastase 1 In Lung Physiology And in α1-Antitrypsin Deficiency
Rashika Joshi, Andrea Heinz, Qiang Fan…·Brian M. Varisco
This study shows Cela1 is responsible for stretch-inducible lung elastase activity and is required for emphysema in AAT deficiency, with conserved features in placental mammals.
DOI 10.1101/138776