Molecular BiologyInternational Journal of Molecular SciencesPeer-reviewed
Dysfunctional Mitochondria in Cardiac Fibers of a Williams-Beuren Syndrome Mouse Model
Noura Abdalla, Ester Tobías-Baraja, Alejandro Gonzalez…·Victoria Campuzano
This study examines mitochondrial dysfunction in a Williams-Beuren Syndrome mouse model, finding altered mitochondrial dynamics and respiratory chain dysfunction in cardiac fibers, similar to human WBS fibroblasts.
3 citations