BiochemistrybioRxiv
Defective Function of α-Ketoglutarate Dehydrogenase Exacerbates Mitochondrial ATP Deficits during Complex I Deficiency
G. G. Piroli, A. M. Manuel, R. S. McCain…·N. Frizzell
This study shows that defective α-ketoglutarate dehydrogenase function worsens mitochondrial ATP deficits in Complex I deficiency by impairing TCA cycle components.
DOI 10.1016/j.redox.2023.102932