HOIL-1L deficiency induces cell cycle alteration which causes immaturity of myocyte and fibrogenesis
K. Akagi, S. Baba, H. Fujita…·J. Takita
This study shows HOIL-1L deficiency leads to cell cycle defects and fibrosis in myotubes and cardiomyocytes, contributing to myopathy and dilated cardiomyopathy.