BiochemistrybioRxiv
DHTKD1 and OGDH display in vivo substrate overlap and form a hybrid ketoacid dehydrogenase complex
J. Leandro, T. Dodatko, J. Aten…·S. M. Houten
The paper shows DHTKD1 and OGDH share in vivo substrate overlap and form a hybrid ketoacid dehydrogenase complex, with implications for GA1 therapy.
DOI 10.1093/hmg/ddaa037