Cell BiologyJCI InsightPeer-reviewed
Dysregulated alveolar epithelial cell progenitor function and identity in Hermansky-Pudlak syndrome
Joanna Y. Wang, Sylvia N. Michki, Sneha Sitaraman…·Lisa R. Young
This study identifies intrinsic AT2 progenitor dysfunction and p53 pathway dysregulation as novel mechanisms driving pulmonary fibrosis in Hermansky-Pudlak syndrome.
10 citations