SPNS1 is required for the transport of lysosphingolipids and lysoglycerophospholipids from lysosomes
H. T. T. Ha, X. T. A. Nguyen, L. K. Vo…·L. N. Nguyen
This study identifies SPNS1 as a lysosomal transporter critical for exporting lysosphingolipids and lysoglycerophospholipids, linking its deficiency to lysosomal storage disease-like pathology.